Outcomes of lung transplantation for idiopathic pleuroparenchymal fibroelastosis.
Haruhiko ShiiyaJun NakajimaHiroshi DateToyofumi Fengshi Chen-YoshikawaKiminobu TanizawaTomohiro HandaTakahiro OtoShinji OtaniToshio ShiotaniYoshinori OkadaYasushi MatsudaTakeshi ShiraishiToshihiko MorogaMasato MinamiSoichiro FunakiMasayuki ChidaIchiro YoshinoGo HatachiYukari UemuraMasaaki SatoPublished in: Surgery today (2021)
Despite extrapulmonary problems such as a flat chest, low BMI, and associated restrictive impairment persisting in patients with IPPFE, patient survival after LT for IPPFE or IPF was equivalent.