Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot study.
Marco MaglioneSilvia MontellaCarmine MollicaVincenzo CarnovalePaola IacotucciFabiola De GregorioAntonella ToscoMariarosaria CervasioValeria RaiaFrancesca SantamariaPublished in: Italian journal of pediatrics (2017)
MRI is a valuable radiation-free tool for comparative PCD and CF lung disease assessment. Patients with PCD may exhibit similar MRI and lung function changes as CF subjects with mild pulmonary disease. Delay in PCD diagnosis is unlikely the only determinant of similarities.