Effects of weakness of orofacial muscles on swallowing and communication in FSHD.
Karlien MulKiera N BerggrenMattie Y SillsAyla McCalleyBaziel G M van EngelenNicholas E JohnsonJeffrey M StatlandPublished in: Neurology (2019)
Cheek compression strength is the most sensitive IOPI measure for orofacial weakness in FSHD. Orofacial weakness contributes to dysphagia and speech difficulties in FSHD, which are both common, though generally mild. Higher endurance of orofacial muscles was associated with a lower chance of dysphagia or speech problems. More research is required for further refinement of the pattern of facial muscle involvement in FSHD and to provide new insights for improvement of speech and language therapy.