Glycomacropeptide: long-term use and impact on blood phenylalanine, growth and nutritional status in children with PKU.
Anne DalyS EvansS ChahalS SantraA PintoR JacksonC GingellJ RochaF J Van SpronsenA MacDonaldPublished in: Orphanet journal of rare diseases (2019)
CGMP-AA increases blood Phe concentrations and so it can only be used partly to contribute to protein substitute in some children with PKU. CGMP-AA should be carefully introduced in children with PKU and close monitoring of blood Phe control is essential.
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