The Effects of a Ketogenic Diet on Patients with Dihydrolipoamide Dehydrogenase Deficiency.
Orna Staretz-ChachamBen Pode-ShakkedEyal KristalSmadar Yaala AbrahamKeren PorperOhad WormserIlan ShelefYair AniksterPublished in: Nutrients (2021)
The use of KD offers an advantage regarding survival; however, there is no significant improvement in QOL.