Comparison of Lesional Juvenile Myositis and Lupus Skin Reveals Overlapping Yet Unique Disease Pathophysiology.
Jessica L TurnierLauren M PachmanLori LoweLam C TsoiSultan ElhajRajasree MenonMaria C AmorusoGabrielle A MorganJohann E GudjonssonCeline C BerthierJ Michelle KahlenbergPublished in: Arthritis & rheumatology (Hoboken, N.J.) (2021)
Lesional juvenile myositis skin demonstrates a striking IFN signature similar to that previously reported in juvenile myositis muscle and peripheral blood. Further investigation into the association of a higher IFN score with NXP-2 autoantibodies may provide insight into disease endotypes and pathogenesis.