Paediatric cardiomyopathies: echocardiographic diagnosis, clinical profile, and demographic characteristics: the experience of a tertiary referral centre for Latin American paediatric cardiology.
Víctor M Huertas-QuiñonesCamilo F MestraValeria Peña-TrujilloSebastian Gallo-BernalMariana VillavecesLaura C Alarcón-ForeroPublished in: Cardiology in the young (2020)
From a total of 29,533 children who attended our institution during the study period, 89 new cases of primary cardiomyopathies were identified. The median age at diagnosis was 11 years (interquartile range 4-9). Dilated cardiomyopathy accounted for 57.3% (n = 51) of cases; hypertrophic cardiomyopathy, 12.3% (n = 11); restrictive cardiomyopathy, 8.9% (n = 8); non-compacted cardiomyopathy, 7.8% (n = 7); arrhythmogenic ventricular cardiomyopathy, 6.7% (n = 6); and unspecified cardiomyopathy, 6.7% (n = 6). Heart failure was observed in 53.93% of the patients. The overall mortality was 12.36% (n = 11), which included two of eight patients who underwent cardiac transplantation.
Keyphrases
- heart failure
- left ventricular
- end stage renal disease
- ejection fraction
- hypertrophic cardiomyopathy
- newly diagnosed
- chronic kidney disease
- intensive care unit
- emergency department
- peritoneal dialysis
- primary care
- young adults
- stem cells
- type diabetes
- pulmonary hypertension
- risk factors
- atrial fibrillation
- mesenchymal stem cells
- mitral valve
- acute kidney injury
- patient reported outcomes
- cardiac resynchronization therapy
- patient reported