Anti-nuclear matrix protein 2 antibody-positive inflammatory myopathies represent extensive myositis without dermatomyositis-specific rash.
Yuki IchimuraRisa KonishiMiwako ShoboSae InoueMari OkuneAkemi MaedaRyota TanakaNoriko KubotaIsao MatsumotoAkiko IshiiAkira TamaokaAsami ShimboMasaaki MoriTomohiro MorioTakayuki KishiTakako MiyamaeJantima TanboonMichio InoueIchizo NishinoManabu FujimotoToshifumi NomuraHanako Koguchi-YoshiokaPublished in: Rheumatology (Oxford, England) (2021)
Anti-NXP2 antibody-positive IIMs, which include dermatomyositis sine dermatitis, are characterised by atypical skin manifestations and extensive muscular involvement.