The role of liver transplantation in COACH syndrome (Joubert syndrome with congenital hepatic fibrosis): A review of the literature.
Lijian ChenHajime UchidaRyuji KomineTasuku KodamaToshimasa NakaoNoriki OkadaYusuke YanagiSeiichi ShimizuSyed AbbasAkinari FukudaSeisuke SakamotoMureo KasaharaPublished in: Pediatric transplantation (2023)
LT should be considered an effective treatment for COACH syndrome in patients with severe portal hypertension. However, a detailed follow-up of the renal function is necessary.