Pulmonary Manifestations and Progression of Lung Disease in Juvenile-onset Mixed Connective Tissue Disease.

Siri Opsahl HetlevikBerit FlatøTrond Mogens AaløkkenMay Brit LundSilje ReiseterGeorg Karl MynarekEllen NordalMarite RyggVibke Lilleby

Published in: The Journal of rheumatology (2018)

Compared to controls, patients with JMCTD had impaired pulmonary function. ILD was present in 27% of patients after a mean 16 years of disease duration, mostly as mild disease, and did not progress. ILD seems to be less common in juvenile-onset than in adult-onset MCTD, and ILD in JMCTD seems mostly mild and stable over time.

Keyphrases

interstitial lung disease
end stage renal disease
chronic kidney disease
idiopathic pulmonary fibrosis
patient reported