Extra-axial sacral soft tissue giant cell ependymoma affecting a child: Case report and review of the literature.
Silvia PlanasOfelia CruzMiguel BejaranoAsteria AlbertCarlota RoviraJosep A BombiPublished in: Neuropathology : official journal of the Japanese Society of Neuropathology (2021)
An otherwise healthy eight-year-old girl presented with a mass in the soft tissue of the sacral region. The lesion was diagnosed as a vascular malformation on imaging studies, for which percutaneous sclerotherapy was attempted. The mass continued to grow and a complete resection was performed after four years. The pathological diagnosis was giant cell ependymoma (GCE). GCE is a term used to describe a rare histologic variant of ependymoma characterized by malignancy-like morphologic phenotype and indolent behavior. To the best of our knowledge, this is the first case of extra-axial soft tissue sacral GCE reported in a child.