Estimation of Ambulation and Survival in Neurodegeneration with Brain Iron Accumulation Disorders.
Elahe AminiMohammad RohaniAnthony E LangZahra AzadSeyed Amir Hassan HabibiAfagh AlaviGholam Ali ShahidiMaziar EmamikhahAhmad ChitsazPublished in: Movement disorders clinical practice (2023)
KRS had the best survival with the most extended ambulation period. The classical PKAN and MPAN cases had similar progression patterns to loss of ambulation ability, while MPAN patients had a slower progression to death. Spasticity was revealed to be the most determining factor for death.