Primary Occlusive Panvasculitis with Segmental Periarterial Plaques.

Both patients presented with findings of bilateral panvasculitis with prominent segmental periarterial plaques and had repeated episodes of vascular occlusions before corticosteroid and immunosuppressants treatment, after which no additional occlusions were observed. We propose the constellation of findings constitute a novel clinical entity, occlusive panvasculitis with segmental periarterial plaques.