Prenatal Diagnosis of Primrose Syndrome.
Wael AbdallahEmmanuel SpaggiariSophie BrissetRodolphe DardTania Attié BitachJean Philippe BaultThibault QuibelPublished in: Journal of ultrasound in medicine : official journal of the American Institute of Ultrasound in Medicine (2023)
Primrose syndrome is a very rare congenital malformation. Symptoms of this disorder may appear during childhood, but the diagnosis is identified in adulthood in the majority of cases. The prenatal diagnosis of Primrose syndrome is not developed in the literature. We present herein a case series of 3 cases with characteristic sonographic features. A dysmorphic metopic suture, downslanting palpebral fissures, a wide forehead, and agenesis of corpus callosum are the main signs. A missense mutation in ZBTB20 identified in whole exome sequencing can confirm the prenatal diagnosis of Primrose syndrome.