Cardiac device implantation and device usage in Fabry and hypertrophic cardiomyopathy.
Ravi VijapurapuWilliam BradlowFrancisco LeyvaJames C MoonAbbasin ZegardNigel LewisD KotechaAna JovanovicDerralynn A HughesPeter WoolfsonRichard P SteedsTarekegn GeberhiwotPublished in: Orphanet journal of rare diseases (2022)
This study demonstrates arrhythmia burden and ICD usage in FD is high, suggesting that Fabry cardiomyopathy may be more 'arrhythmogenic' than previously thought. Existing risk models cannot be mutually applicable and further research is needed to provide clarity in managing Fabry patients with cardiac involvement.