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A lymphocyte-mediated cause of secondary PAP.

Bruce C Trapnell
Published in: Blood (2015)
In this issue of Blood, Iriguchi et al report that T-lymphocyte–restricted overexpression of T-bet causes a maturational arrest in mononuclear phagocyte lineage cells and severe secondary pulmonary alveolar proteinosis (PAP).
Keyphrases
  • peripheral blood
  • induced apoptosis
  • cell cycle arrest
  • pulmonary hypertension
  • cell proliferation
  • cell cycle
  • transcription factor
  • endoplasmic reticulum stress
  • signaling pathway
  • pi k akt