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Assessment of Left Ventricular Myocardial Fibrosis in Adult Patients With Ebstein Anomaly: A Retrospective Cohort Study Based on Cardiac Magnetic Resonance and Histopathological Samples.

Valente Fernandez-BadilloJavier Serrano-RomanNeftalí Eduardo Antonio-VillaAldo Cabello-GanemAdrian Espejel-GuzmanLaura Victoria Torres-AraujoAlberto Aranda-FraustroRoberto Cano-ZarateEnrique Solorzano-PinotCandace KeirnsAloha Meave-GonzalezErick Alexanderson-RosasNilda Espinola-Zavaleta
Published in: Circulation. Cardiovascular imaging (2023)
There is a high prevalence of LV fibrosis replacement in adults with Ebstein anomaly, characterized by specific CMR and histological patterns. Furthermore, LV-LGE fibrosis is an independent predictor of cardiovascular disease mortality, which could be integrated into risk assessment in clinical management.
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