A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle.
Irene RasoAndrea QuartiMassimo ChessaDomenica Paola BasileAntonio SaracinoAngelo Fabio D'AielloClaudia RaineriMario CarminatiAlessandro GiambertiPublished in: World journal for pediatric & congenital heart surgery (2020)
Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.
Keyphrases
- congenital heart disease
- catheter ablation
- pulmonary artery
- mitral valve
- left ventricular
- atrial fibrillation
- heart failure
- vena cava
- left atrial
- inferior vena cava
- pulmonary hypertension
- left atrial appendage
- aortic valve
- case report
- coronary artery
- aortic stenosis
- pulmonary arterial hypertension
- transcatheter aortic valve replacement
- machine learning
- deep learning
- high speed
- neural network