20-year follow-up study of Danish HHT patients-survival and causes of death.
Anette Drøhse KjeldsenKatrine Saldern AagaardPernille Mathiesen TørringSören MöllerAnders GreenPublished in: Orphanet journal of rare diseases (2016)
The mortality was not increased among Danish HHT patients compared to controls. This study is based on a clinical unselected series of HHT patients with the whole spectrum of severity, independent of need for medical care. Our data also suggest that HHT patients to a lesser degree than the background population are affected by cancer.