Respiratory Function and Sleep Disordered Breathing in Pediatric Duchenne Muscular Dystrophy.

Alberto Andrea Zambon Federica Trucco Aidan LavertyMollie RileyDeborah RidoutAdnan Y ManzurFrancois Abel Francesco Muntoni

Published in: Neurology (2022)

FVC% <50 was associated with NH in close to a third of patients. CO2 elevation can be associated with obstructive/pseudo-obstructive events and was also observed in early nonambulant cases or in the presence of FVC >50%. These results are relevant for the clinical management of SDB.

Keyphrases

duchenne muscular dystrophy
end stage renal disease
ejection fraction
peritoneal dialysis
prognostic factors
patient reported outcomes
room temperature
respiratory tract