Birmingham epidermolysis severity score and vitamin D status are associated with low BMD in children with epidermolysis bullosa.
G RodariS GuezF ManzoniK K ChalouhiE ProfkaS BergamaschiS SaleraG TadiniF M UlivieriA SpadaClaudia GiavoliS EspositoPublished in: Osteoporosis international : a journal established as result of cooperation between the European Foundation for Osteoporosis and the National Osteoporosis Foundation of the USA (2016)
Low aBMD can be considered a systemic complication of EB, primarily associated with BEBS score and 25-hydroxyvitamin D levels. Therefore, longitudinal evaluation of bone status is ongoing in these patients to define whether vitamin D supplementation would prevent, or at least reduce, bone status impairment.