Patient powered prophylaxis: A 12-month study of individualized prophylaxis in adults with severe haemophilia A.

Haowei Linda SunKam A McIntoshSandra J SquireMing YangClaude BartholomewDeb S GuePat G CampShannon C Jackson

Published in: Haemophilia : the official journal of the World Federation of Hemophilia (2017)

Patients with SHA who switched from standard to individualized prophylaxis show reduced ABR and increased FVIII consumption, and also improved their health-related quality of life. The mechanism is independent of adherence to prescribed prophylactic regimen.

Keyphrases

case report
early onset
type diabetes
metabolic syndrome
drug induced
skeletal muscle