A FBN1 variant manifesting as non-syndromic ectopia lentis with retinal detachment: clinical and genetic characteristics.
Kirk A J StephensonAdrian DockeryMichael O'KeefeAndrew GreenG Jane FarrarDavid J KeeganPublished in: Eye (London, England) (2019)
The FBN1 variant described herein confers an increased risk of both EL and RRD and can now be upgraded to 'pathogenic' ACMG status.