Modifiable factors affecting renal preservation in type I glycogen storage disease after liver transplantation: a single-center propensity-match cohort study.
Yi-Chia ChanKai-Min LiuChao-Long ChenAldwin D OngChih-Che LinChee-Chien YongPei-Chun TsaiLiang-Suei LuJer-Yuarn WuPublished in: Orphanet journal of rare diseases (2021)
Post-LT renal function was well-preserved in most GSD-I patients. Early initiation of cornstarch therapy before preschool age, followed by LT, achieved a good renal prognosis.