Pulmonary Manifestations of the Autoimmune Lymphoproliferative Syndrome. A Retrospective Study of a Unique Patient Cohort.
Chuen-Yen LauAndrew D MihalekJing WangLori E DoddKatie PerkinsSusan PriceSharon WebsterStefania PittalugaLes R FolioV Koneti RaoKenneth N OlivierPublished in: Annals of the American Thoracic Society (2018)
Patients with ALPS can develop chest radiographic findings with protean manifestations that may mimic pulmonary infection. Management of patients with ALPS with incidental lung lesions identified by CT imaging should be guided by clinical correlation. Symptomatic patients may benefit from chest CT imaging and lesion biopsy to exclude infection and guide administration of immunosuppressive therapy.
Keyphrases
- end stage renal disease
- high resolution
- pulmonary hypertension
- computed tomography
- image quality
- contrast enhanced
- newly diagnosed
- case report
- ejection fraction
- chronic kidney disease
- dual energy
- multiple sclerosis
- peritoneal dialysis
- magnetic resonance imaging
- positron emission tomography
- stem cells
- patient reported outcomes
- magnetic resonance
- ultrasound guided
- fluorescence imaging
- patient reported