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Concomitant Wilms tumor and autosomal dominant polycystic kidney disease.

Andrew M FlemingDaniel B GehleMelissa R PerrinoDylan E GraetzJohn J BisslerElizabeth B McCarvilleMatthew J KrasinRachel C BrennanJinghui ZhangWentao YangYadav SapkotaMelissa M HudsonAndrew M DavidoffDaniel M GreenAndrew Jackson Murphy
Published in: Pediatric blood & cancer (2024)
Concomitant inheritance of ADPKD and development of WT are extremely rare, and manifestations of ADPKD may not present until late childhood or adulthood. ADPKD is not a known predisposing condition for WT. When ADPKD diagnosis is made by family history, imaging, and/or genetic testing before WT diagnosis and treatment, the need for extensive preoperative characterization of cystic kidney lesions in children and increased risk of post-nephrectomy kidney failure warrant further discussion of surgical approach and perioperative management strategies.
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