Characterization of CT scans of patients with Birt-Hogg-Dubé syndrome compared with those of Chinese patients with non-BHD diffuse cyst lung diseases.
Wenshuai XuZhiyan XuYaping LiuYongzhong ZhanXin SuiRuie FengMin PengXue LiJun WangShuzhen MengLi WangXinlun TianXue ZhangKai-Feng XuPublished in: Orphanet journal of rare diseases (2020)
The pulmonary cysts in patients with BHD tended to be fusiform, less numerous and located predominantly in the lower lobe and near the mediastinum. These radiologic pulmonary features could assist physicians in differentiating BHD from other DCLDs.