Leptomeningeal Interfoliar Enhancement on Vessel Wall MR Imaging as a Unique Radiologic Finding of Susac Syndrome.
P CardozoMariano MarrodanA GilmoreM P FiolHernán ChavesPublished in: AJNR. American journal of neuroradiology (2023)
Susac syndrome is a rare disorder affecting the brain, retina, and inner ear, probably triggered by an immune-mediated endotheliopathy. Diagnosis is based on clinical presentation and ancillary test findings (brain MR imaging, fluorescein angiography, and audiometry). Recently, vessel wall MR imaging has shown increased sensitivity in the detection of subtle signs of parenchymal, leptomeningeal, and vestibulocochlear enhancement. In this report, we describe a unique finding identified using this technique in a series of 6 patients with Susac syndrome and discuss its potential value for diagnostic work-up and follow-up.
Keyphrases
- contrast enhanced
- case report
- white matter
- computed tomography
- resting state
- optical coherence tomography
- cerebrospinal fluid
- magnetic resonance imaging
- multiple sclerosis
- magnetic resonance
- small cell lung cancer
- diabetic retinopathy
- cerebral ischemia
- quantum dots
- blood brain barrier
- subarachnoid hemorrhage
- optic nerve