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C3 glomerulopathy in cystic fibrosis: a case report.

Domenico SantoroRossella SiligatoCarmela VadalàMariacristina LucantoSimona CristadoroGiovanni ContiMichele BuemiStefano CostaEttore SabadiniGiuseppe Magazzù
Published in: BMC nephrology (2018)
The co-existence of C3 glomerulopathy in a patient with CF, which is characterized by chronic infection/inflammation, makes this case an interesting model of chronic altered systemic activation of the alternative pathway of the complement cascade.
Keyphrases
  • cystic fibrosis
  • pseudomonas aeruginosa
  • oxidative stress
  • lung function