Outcome and prognostic factors in pediatric malignant peripheral nerve sheath tumors: An analysis of the European Pediatric Soft Tissue Sarcoma Group (EpSSG) NRSTS-2005 prospective study.
Max M Van NoeselDaniel OrbachBernadette BrennanAnna KelseyIlaria ZanettiGian Luca de SalvoMark N GazeRoss J CraigieKieran McHughNadine FrancottePaola ColliniGianni BisognoMichela CasanovaAndrea C FerrariPublished in: Pediatric blood & cancer (2019)
The outcome for patients with resectable MPNST was excellent. Standard ifosfamide-doxorubicin for unresectable MPNST rendered the best reported outcome. Children with NF1 disease seem to have worse prognosis.