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Atrial Flutter in PRKAG2 Syndrome: Clinical and Electrophysiological Characteristics.

Eduardo Faria Soares de MagalhãesLuiz Pereira de MagalhãesJussara de Oliveira PinheiroAlex Teixeira GuabiruRoque Aras Júnior
Published in: Arquivos brasileiros de cardiologia (2022)
Patients with PRKAG2 syndrome presented atrial flutter at an earlier age and had fewer comorbidities when compared to patients with atrial flutter without mutation phenotype. The occurrence of atrial flutter in young individuals, especially in the presence of ventricular preexcitation and familial ventricular hypertrophy, should raise the suspicion of PRKAG2 syndrome.
Keyphrases
  • catheter ablation
  • atrial fibrillation
  • left atrial
  • heart failure
  • case report
  • left ventricular
  • early onset