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IgM monoclonal gammopathy with heavy-and-light-chain amyloidosis resembling fibrillary glomerulonephritis determined by tandem mass spectrometry: a case report.

Misa AdachiMineaki KitamuraKumiko MutaAkihiro MaekawaTadashi UramatsuMasato TadokoroSatoshi FunakoshiSatoshi HisanoNaomi KuwaharaAkira ShimizuHiroshi MukaeTomoya Nishino
Published in: BMC nephrology (2020)
We reported a case of μ and κ chain AHL resembling FGN requiring LMD/MS for definitive diagnosis. Since FGN and amyloidosis exhibit pathological findings, even if Congo red staining is positive, LMD/MS needs to be considered in cases atypical pathological findings, such as silver stain positivity or thicker fibrils.
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