Clinical characteristics and risk stratification of desmoplakin cardiomyopathy.
Weijia WangBrittney MurrayCrystal TichnellNisha A GilotraStefan L ZimmermanAlessio GasperettiPaul ScheelHarikrishna TandriHugh CalkinsCynthia A JamesPublished in: Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology (2021)
DSP cardiomyopathy affects both ventricles and carries high risk for ventricular arrhythmia and heart failure. Myocardial injury is associated with worse disease outcomes. Both diagnosis and risk stratification of DSP cardiomyopathy need refinement.