Measuring cognitive impairment and monitoring cognitive decline in Huntington's disease: a comparison of assessment instruments.
Andrea Horta-BarbaSaul Martinez-HortaJesús Pérez-PérezArnau Puig-DaviNatascia de LuciaGiuseppe de MicheleElena SalvatoreStefanie KehrerJosef PrillerSimone MiglioreFerdinando SquitieriAnna CastaldoCaterina MariottiVeronica MañanesJose Luis Lopez-SendonNoelia RodriguezAsunción Martinez-DescalsFilipa JúlioCristina JanuárioMarianna DelussiMarina de TommasoSandra NogueraJesús Ruiz-IdiagoEmilia J SitekRenata WallnerAngela NuzziJavier PagonabarragaJaime Kulisevskynull nullPublished in: Journal of neurology (2023)
The PD-CRS is a valid and reliable instrument to capture MCI and dementia syndromes in HD. It captures the different trajectories of cognitive progression as a function of cognitive status and shows sensitivity to change in MCI and dementia.