Cystic fibrosis dermatitis arthritis syndrome: A series of four cases.
Gabrielle SchwartzmanBarrett J ZlotoffAlejandro A GruDarren J GuffeyPublished in: Pediatric dermatology (2024)
Dermatologic manifestations of cystic fibrosis (CF) include nutrient deficiency dermatoses, vasculitis, transient reactive papulotranslucent acrokeratodema, digital clubbing, and increased rates of atopy and drug reactions. Few cases of a characteristic eruption in patients with episodic arthritis of CF have been described with prior reports primarily occurring outside of the dermatology literature. We report four cases consistent with this presentation to add to the literature and propose a new and unifying name to recognize this entity as cystic fibrosis dermatitis arthritis syndrome (CF-DAS). Clinical suspicion should remain high in young female patients with cystic fibrosis presenting with episodic joint pain and rash, independent of pulmonary exacerbations.
Keyphrases
- cystic fibrosis
- pseudomonas aeruginosa
- rheumatoid arthritis
- lung function
- case report
- systematic review
- end stage renal disease
- ejection fraction
- chronic kidney disease
- newly diagnosed
- chronic pain
- disease activity
- pulmonary hypertension
- adverse drug
- prognostic factors
- pain management
- systemic lupus erythematosus
- chronic obstructive pulmonary disease
- spinal cord
- replacement therapy
- electronic health record