Early NIV is associated with accelerated lung function decline in Duchenne muscular dystrophy treated with glucocorticosteroids.

Megan E AnglissKiara D SclipLeanne M Gauld

Published in: BMJ open respiratory research (2021)

Overall, LF decline is reduced on NIV. Steroid Naïve patients have lower LF and faster decline, which slows following NIV initiation. An accelerated LF decline was seen on NIV in Steroid Users which requires further prospective research.

Keyphrases

lung function
duchenne muscular dystrophy
newly diagnosed
end stage renal disease
cystic fibrosis
chronic obstructive pulmonary disease
ejection fraction
chronic kidney disease
air pollution
patient reported