Adult-onset idiopathic peripheral pulmonary artery stenosis.

Yudai Tamura Yuichi TamuraAyako ShigetaKazuya HosokawaYu TaniguchiTakumi InamiShiro AdachiIchizo TsujinoNaohiko NakanishiKimi SatoJiro SakamotoNobuhiro TanabeNoriaki TakamaKazuto NakamuraKayoko KubotaNaohiro KomuraShigehiko KatoJun YamashitaMakoto TakeiShuji JohoShunsuke IshiiRyo TakemuraKoichiro Sugimura Koichiro Tatsumi

Published in: The European respiratory journal (2023)

In this study, the patients with adult-onset idiopathic PPS presented with segmental and peripheral pulmonary artery stenosis. Although patients had severe pulmonary hypertension at baseline, they showed a favorable treatment response to the PAH-drugs combined with transcatheter pulmonary angioplasty.

Keyphrases

pulmonary artery
pulmonary hypertension
pulmonary arterial hypertension
coronary artery
end stage renal disease
ejection fraction
newly diagnosed
prognostic factors
peritoneal dialysis
patient reported outcomes
early onset
chemotherapy induced
combination therapy
patient reported