Hermansky-Pudlak syndrome-associated pneumothorax with rapid progression of respiratory failure: a case report.

Yukari KatoMotoyasu KatoHiroaki IharaEri HayakawaKohei ShibayamaKeita MiuraTomoko YamadaYoichiro MitsuishiTakehito ShukuyaJun ItoTakeshi MatsunagaTadashi SatoKenji SuzukiKazuhisa Takahashi

Published in: BMC pulmonary medicine (2020)

We herein report the case of a rare HPS patient who developed pneumothorax with progressive PF. Pneumothorax may cause rapid progressive respiratory failure and may be associated with PF progression in HPS-PF.

Keyphrases

respiratory failure
extracorporeal membrane oxygenation
multiple sclerosis
mechanical ventilation
case report
loop mediated isothermal amplification
acute respiratory distress syndrome
intensive care unit