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C4 nephritic factor in patients with immune-complex-mediated membranoproliferative glomerulonephritis and C3-glomerulopathy.

Nóra GaramZoltán ProhászkaÁgnes SzilágyiChristof AignerAlice SchmidtMartina GagglGere Sunder-PlassmannDóra BajcsiJürgen BrunnerAlexandra DumfarthDaniel CejkaStefan FlaschbergerHana FlögelovaÁgnes HarisÁgnes HartmannAndreas HeilosThomas MuellerKrisztina RusaiKlaus ArbeiterJohannes HoferDániel JakabMária SinkóErika SzigetiCsaba BereczkiViktor JankoKata KelenGyörgy S ReuszAttila J SzabóNóra KlenkKrisztina KóborNika KojcMaarten KnechtelsdorferMario LaganovicAdrian Catalin LunguAnamarija MeglicRina RusTanja Kersnik-LevartErnesta MacionieneMarius MiglinasAnna PawłowskaTomasz StompórLudmila PodrackaMichael RudnickiGert Mayernull Romana RysavaJana ReiterovaMarijan Saraganull Tomáš SeemanJakub ZiegEva SládkováTamás SzabóAndrei CapitanescuSimona StancuMiroslav TisljarKresimir GalesicAndrás TislérInga VainumäeMartin WindpesslTomas ZaoralGalia ZlatanovaDorottya Csuka
Published in: Orphanet journal of rare diseases (2019)
In conclusion, C4NeF may be a possible cause of complement dysregulation in approximately 10-15% of IC-MPGN/C3G patients.
Keyphrases
  • end stage renal disease
  • ejection fraction
  • newly diagnosed
  • chronic kidney disease
  • peritoneal dialysis