Impairment of respiratory muscle strength in Berardinelli-Seip congenital lipodystrophy subjects.
Jorge Luiz Dantas de MedeirosBruno Carneiro BezerraThiago Anderson Brito de AraújoAquiles Sales Craveiro SarmentoLázaro Batista de Azevedo MedeirosLucien Peroni GualdiMaria do Socorro Luna CruzThaiza Teixeira Xavier NobreJosivan Gomes LimaJulliane Tamara Araújo de Melo CamposPublished in: Respiratory research (2018)
BSCL subjects showed lower respiratory muscle strength when compared with healthy subjects; however, PMS was not altered. These findings were maintained at similar levels during the two years of evaluation. Our data reveal the first association of BSCL with the development of respiratory muscle weakness.