Scleroderma renal crisis: observations from the South Australian Scleroderma Register.
Yassmin KhadraJennifer G WalkerPaul HakendorfSusanna M ProudmanMaureen RischmuellerCatherine L HillSamuel L WhittleEliza K PontifexPeter J Roberts-ThomsonPublished in: Internal medicine journal (2021)
SRC is a rare occurrence with an incidence of 0.58/million/year in South Australia. This frequency has not changed over time. It continues to have a severe adverse outcome with frequent requirement for renal replacement therapy and poor survival. Nailfold capillaroscopy revealed evidence of extensive capillary damage. No improvement in survival was observed over the 34-year study period.