Phenotypic analysis of pyrin-associated autoinflammation with neutrophilic dermatosis patients during treatment.
Erika Van NieuwenhoveVeerle IdeJames DooleyJoost Van Den OordMohammad ShahrooeiNima ParvanehVahid ZiaeeSinisa SavicMark KacarXavier BossuytStephanie Humblet-BaronAdrian ListonCarine WoutersPublished in: Rheumatology (Oxford, England) (2021)
In our experience, while anakinra appears safe, it was not superior to biologicals targeting TNF-α in PAAND despite evidence directly implicating dysregulated IL-1β signalling.