Extrapulmonary manifestations of a telomere syndrome in patients with idiopathic pulmonary fibrosis are associated with decreased survival.
Thijs W HoffmanJoanne J van der VisDouwe H BiesmaJan C GruttersColine H M van MoorselPublished in: Respirology (Carlton, Vic.) (2022)
Taking a careful clinical and family history focused on extrapulmonary manifestations of a telomere syndrome can provide important prognostic information in patients with IPF, as this is associated with shorter survival.