Improved Survival for Patients with Systemic Sclerosis-associated Pulmonary Arterial Hypertension: The Johns Hopkins Registry.
Hussein J HassanMario NaranjoNour AyoubTraci HoustenSteven HsuAparna BalasubramanianCatherine E SimpsonRachel L DamicoStephen C MathaiTodd M KolbPaul M HassounPublished in: American journal of respiratory and critical care medicine (2022)
This is the largest single-center study that compares clinical characteristics of SSc-PH patients between the last two decades. Transplant-free survival has improved significantly for those with Group 1 disease over the last decade, possibly secondary to earlier detection and better therapeutic management. Conversely, those with Group 2 or 3 disease continue to have dismal prognosis.