Outcomes After Development of Ventricular Arrhythmias in Single Ventricular Heart Disease Patients With Fontan Palliation.
Heather M GiaconeHenry ChubbAnne M DubinKara S MotonagaScott R CeresnakWilliam Rowland GoodyerDeb HanishAnthony V TrelaNicole BoramanandErin LencioniDerek B BoothroydAnna Graber-NaidichGail WrightChristiane L HaeffeleSeth A HollanderDoff B McElhinneyMichael MaFrank L HanleySharon ChenPublished in: Circulation. Arrhythmia and electrophysiology (2023)
Ventricular arrhythmias occurred in 11% of Fontan patients and was highly associated with transplant or death, with a transplant-free survival of <50% at 5-year post-VA diagnosis. Risk factors for VA included older age at Fontan and history of right ventricular to pulmonary artery conduit. A diagnosis of VA in Fontan patients should prompt increased clinical surveillance.