Surgery on a dilated aorta associated with a connective tissue disease or inflammatory vasculitis in children and adolescents.
Jae Gun KwakWoong-Han KimEung Re KimYoon Jin KangJooncheol MinJae Hong LimYong Jin KimPublished in: Cardiology in the young (2019)
Cases of surgical treatment for a dilated aorta associated with a connective tissue disease and inflammatory vasculitis are rare in children and adolescents at our institution. Most of the patients in this study showed a tolerable postoperative course. However, the aorta showed progressive dilation over time even after surgical treatment, especially in patients with Loeys-Dietz syndrome. In these patients, close and more frequent regular follow-up is required.