Altered Immune Response in Organic Acidemia.
Ilayda AltunAyca KiykimTanyel ZubariogluNihan BurteceneDuhan HopurcuogluBirol TopcuMehmet Serif CanseverErtugrul KıykımHaluk Cezmi CokugrasAyse Cigdem Aktuglu ZeybekPublished in: Pediatrics international : official journal of the Japan Pediatric Society (2021)
Patients with OAs may show adaptive immune defects rendering them susceptible to infections. Metabolic reprogramming based on nutritional modifications may be a promising therapeutic option in the future.