Lung function decline preceding chronic respiratory failure in spinal muscular atrophy: a national prospective cohort study.

Esther S VeldhoenCamiel A WijngaardeRuben P A van EijkFay-Lynn AsselmanNegina SeddiqiLouise A M OttoMarloes StamInge CuppenRenske I WadmanRoelie M Wösten van AsperenErik H J HulzebosLaura P Verweij van den OudenrijnBart BartelsJasmijn BoezerM GaytantCornelis K van der EntW Ludo van der Pol

Published in: Orphanet journal of rare diseases (2023)

remains low and stable in the years preceding initiation of ventilation. Patients who electively started mechanical ventilation had more restrictive lung function at initiation of ventilation, compared to patients who could not be weaned after surgery or a respiratory tract infection.

Keyphrases

lung function
respiratory failure
mechanical ventilation
respiratory tract
acute respiratory distress syndrome
cystic fibrosis
chronic obstructive pulmonary disease
air pollution
intensive care unit
extracorporeal membrane oxygenation
quality improvement
drug induced