Successful Medical-Surgical Management of Intracardiac Thrombosis and Pulmonary Pseudoaneurysms in an Adolescent With Hughes-Stovin Syndrome.
D Sofia Villacis-NunezZachary WestAdil Y KhanFred RodriguezAndi L ShaneHeather RyttingSubhadra ShashidharanMatthew S CliftonGary WoodsMartha ClabbySampath PrahaladPublished in: Journal of investigative medicine high impact case reports (2023)
We present an adolescent male with a single intracardiac mass and pulmonary emboli, complicated by peripheral venous thrombosis and subsequent development of pulmonary pseudoaneurysms, leading to diagnosis of Hughes-Stovin syndrome. Remission was achieved with cyclophosphamide, corticosteroids, and pseudoaneurysm resection and maintained with infliximab and methotrexate.