Treatment adherence in tyrosinemia type 1 patients.
Domingo González-LamuñoPaula Sánchez-PintosFernando AndradeMaria-Luz CouceLuís Aldámiz-EchevarríaPublished in: Orphanet journal of rare diseases (2021)
Despite initially poor adherence to pharmacological and especially dietary treatment among HT1 patients, positive reinforcement at medical consultations resulted in a marked improvement in NTBC levels, indicating the importance of systematic positive reinforcement at medical visits.