Treatment adherence in tyrosinemia type 1 patients.

Domingo González-LamuñoPaula Sánchez-PintosFernando AndradeMaria-Luz CouceLuís Aldámiz-Echevarría

Published in: Orphanet journal of rare diseases (2021)

Despite initially poor adherence to pharmacological and especially dietary treatment among HT1 patients, positive reinforcement at medical consultations resulted in a marked improvement in NTBC levels, indicating the importance of systematic positive reinforcement at medical visits.

Keyphrases

end stage renal disease
newly diagnosed
ejection fraction
chronic kidney disease
healthcare
peritoneal dialysis
prognostic factors
type diabetes
adipose tissue
patient reported outcomes
general practice